1.
Mt Sinai J Med
; 68(4-5): 326-30, 2001.
Artigo
em Inglês
| MEDLINE
| ID: mdl-11514920
RESUMO
Combined immunodeficiency disorders are characterized by abnormalities in cellular and humoral immunity. This classification includes common variable immunodeficiency (CVI), a primary immunodeficiency disorder characterized by hypogammaglobulinemia, recurrent bacterial infections, and significant T-cell abnormalities. Associated autoimmune diseases include rheumatoid arthritis, pernicious anemia, idiopathic thrombocytopenic purpura, and systemic lupus erythematous. Granulomatous lesions in lymphoid tissues, solid organs, and skin have been reported. We describe a patient with CVI who developed cutaneous granulomas with perineural invasion; to our knowledge, this is a previously undescribed feature.
Assuntos
Imunodeficiência de Variável Comum/congênito , Imunodeficiência de Variável Comum/complicações , Granuloma/diagnóstico , Hanseníase Tuberculoide/diagnóstico , Dermatopatias/diagnóstico , Adulto , Diagnóstico Diferencial , Granuloma/etiologia , Humanos , Hanseníase Tuberculoide/etiologia , Masculino , Dermatopatias/etiologia
2.
Int J Dermatol
; 36(12): 881-7, 1997 Dec.
Artigo
em Inglês
| MEDLINE
| ID: mdl-9466191